{"id":69100,"date":"2025-11-14T08:45:52","date_gmt":"2025-11-14T08:45:52","guid":{"rendered":"https:\/\/psychologydictionary.ae\/syndrome-de-gerstmann-streisler-scheinker-gss\/"},"modified":"2025-11-14T08:45:52","modified_gmt":"2025-11-14T08:45:52","slug":"syndrome-de-gerstmann-streisler-scheinker-gss","status":"publish","type":"post","link":"https:\/\/psychologydictionary.ae\/fr\/syndrome-de-gerstmann-streisler-scheinker-gss\/","title":{"rendered":"Syndrome de Gerstmann-Streisler-Scheinker (GSS)"},"content":{"rendered":"<p>Une maladie neurod\u00e9g\u00e9n\u00e9rative h\u00e9r\u00e9ditaire rare caus\u00e9e par une mutation du g\u00e8ne PRNP qui entra\u00eene l\u2019accumulation de prot\u00e9ines prioniques anormales dans le cerveau. La maladie est un type de maladie \u00e0 prions similaire \u00e0 la maladie de Creutzfeldt\u2013Jakob, mais avec une progression plus lente. Le GSS se manifeste g\u00e9n\u00e9ralement \u00e0 l\u2019\u00e2ge m\u00fbr avec des sympt\u00f4mes tels qu\u2019une ataxie progressive, un d\u00e9clin cognitif, une myoclonie (spasmes musculaires), et parfois des changements mentaux. Avec le temps, la maladie entra\u00eene de graves troubles neurologiques et la mort. Il n\u2019existe pas de rem\u00e8de, la th\u00e9rapie vise \u00e0 soulager les sympt\u00f4mes et \u00e0 offrir des soins de soutien.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Une maladie neurod\u00e9g\u00e9n\u00e9rative h\u00e9r\u00e9ditaire rare caus\u00e9e par une mutation du g\u00e8ne PRNP qui entra\u00eene l\u2019accumulation de prot\u00e9ines prioniques anormales dans le cerveau. La maladie est un type de maladie \u00e0 prions similaire \u00e0 la maladie de Creutzfeldt\u2013Jakob, mais avec une progression plus lente. Le GSS se manifeste g\u00e9n\u00e9ralement \u00e0 l\u2019\u00e2ge m\u00fbr avec des sympt\u00f4mes tels [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_bbp_topic_count":0,"_bbp_reply_count":0,"_bbp_total_topic_count":0,"_bbp_total_reply_count":0,"_bbp_voice_count":0,"_bbp_anonymous_reply_count":0,"_bbp_topic_count_hidden":0,"_bbp_reply_count_hidden":0,"_bbp_forum_subforum_count":0,"footnotes":""},"categories":[218],"tags":[],"class_list":["post-69100","post","type-post","status-publish","format-standard","hentry","category-concepts-psychologiques-cles-en-neuropsychologie-clinique"],"_links":{"self":[{"href":"https:\/\/psychologydictionary.ae\/fr\/wp-json\/wp\/v2\/posts\/69100","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/psychologydictionary.ae\/fr\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/psychologydictionary.ae\/fr\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/psychologydictionary.ae\/fr\/wp-json\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/psychologydictionary.ae\/fr\/wp-json\/wp\/v2\/comments?post=69100"}],"version-history":[{"count":0,"href":"https:\/\/psychologydictionary.ae\/fr\/wp-json\/wp\/v2\/posts\/69100\/revisions"}],"wp:attachment":[{"href":"https:\/\/psychologydictionary.ae\/fr\/wp-json\/wp\/v2\/media?parent=69100"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/psychologydictionary.ae\/fr\/wp-json\/wp\/v2\/categories?post=69100"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/psychologydictionary.ae\/fr\/wp-json\/wp\/v2\/tags?post=69100"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}